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Creutzfeldt-Jakob disease
This page provides links to descriptions of activities, reports, news and events, as well as contacts and cooperating partners in the various WHO programmes and offices working on this topic. Also shown are links to related web sites and topics.
MeSH scope note: A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances, personality changes,
ATAXIA;
APHASIA, visual loss, weakness, muscle atrophy,
MYOCLONUS, progressive dementia, and death within one year of disease onset. A familial form exhibiting autosomal dominant inheritance and a new variant
CJD (potentially associated with
ENCEPHALOPATHY, BOVINE SPONGIFORM) have been described. Pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of
PRIONS. (From N Engl J Med, 1998 Dec 31;339(27))
FACT SHEETS
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Bovine spongiform encephalopathy (BSE)
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Variant Creutzfeldt-Jakob disease
RELATED LINKS
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Disease outbreaks: Creutzfeldt-Jakob disease
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Variant Creutzfeldt-Jakob disease
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Prion diseases
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Blood products: Transmissible spongiform encephalopathies (TSE)
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