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Spongiform encephalopathies, Transmissible
This page provides links to descriptions of activities, reports, news and events, as well as contacts and cooperating partners in the various WHO programmes and offices working on this topic. Also shown are links to related web sites and topics.
MeSH scope note: A group of genetic, infectious, or sporadic degenerative human and animal nervous system disorders associated with abnormal
PRIONS. These diseases are characterized by conversion of the normal prion protein to an abnormal configuration via a post-translational process. In humans, these conditions generally feature
DEMENTIA, ataxia, and a fatal outcome. Diseases in this category include
CREUTZFELDT-JAKOB SYNDROME; GERSTMANN-STRAUSSLER-SCHEINKER SYNDROME;
KURU;
SCRAPIE; fatal familial insomnia; bovine spongiform encephalopathy (see
ENCEPHALOPATHY, BOVINE SPONGIFORM); transmissible mink encephalopathy; and chronic wasting disease of mule deer and elk. Pathologic features include a spongiform encephalopathy without evidence of inflammation. The literature occasionally refers to these as unconventional
SLOW VIRUS DISEASES. (From Proc Natl Acad Sci USA 1998 Nov 10;95(23):13363-83)
FACT SHEETS
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Bovine spongiform encephalopathy (BSE)
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Variant Creutzfeldt-Jakob disease
RELATED LINKS
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Disease outbreaks: Creutzfeldt-Jakob disease
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